Turkish Archives of Pediatrics
Case Report

Kikuchi-Fujimoto disease associated with hemophagocytic syndrome

1.

Dr. Behçet Uz Cildren’s Diseases and Surgery Education and Research Hospital, Department of Pediatrics, İzmir, Turkey

2.

Dr. Behçet Uz Cildren’s Diseases and Surgery Education and Research Hospital, Department of Pathology, İzmir, Turkey

Turk Arch Pediatr 2013; 48: 71-73
DOI: 10.4274/tpa.478
Read: 899 Downloads: 697 Published: 08 December 2020

Kikuchi-Fujimoto disease is a rare condition during childhood characterized with fever and cervical lymphadenopathy. Definitive diagnosis of the disease can only be made histologically on lymph node biopsy. Hemophagocytic syndrome associated with Kikuchi-Fujimoto disease is especially rare. In this article, we present a case of an eight years old girl diagnosed as hemophagocytic syndrome associated with KikuchiFujimoto disease. (Turk Arch Ped 2013; 48: 71-3)


Kikuchi-Fujimoto hastalığı ile birlikte hemofagositik sendrom

Kikuchi-Fujimoto hastalığı, ateş ve boyunda lenfadenopati ile nitelenen, çocukluk çağında nadir görülen bir hastalıktır. Hastalığın kesin tanısı sadece histolojik olarak lenf nodu biyopsi ile konulabilir. Kikuchi-Fujimoto hastalığının hemofagositik sendromla birlikteliği çok daha nadirdir. Bu makalede KikuchiFujimoto hastalığıyla birlikte hemofagositik sendrom tanısı alan sekiz yaşındaki kız olgu sunulmuştur. (Türk Ped Arş 2013; 48: 71-3)

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